The presenting features were earache in 16 patients, otorrhea in 7 patients, hearing loss in 5 patients, feeling of aural fullness in 2 patients and EAC mass in 4 patients. The present retrospective study included 23 patients (mean age, 51.4☑5.4 years 12 males) diagnosed with ACC of the EAC between January 2010 and September 2017 at The First Affiliated Hospital of The Third Military Medical University (Chongqing, China). The present study aimed to describe the clinical features and survival of patients with ACC of the EAC. Adenoid cystic carcinoma (ACC) of the external auditory canal (EAC) is a rare tumor.